| Cat# | DIA-763 |
| Descriptions | Lysosomal Alpha-Glucosidase (GAA) is an acid α-glucosidase located in lysosomes that hydrolyzes both α-1,4 and α-1,6 glycosidic bonds in glycogen to release glucose, is the deficient enzyme in Pompe disease, and is the core agent for corresponding enzyme replacement therapy. |
| Applications | Lysosomal Alpha-Glucosidase (GAA) is used for Pompe disease detection kits and glycogen metabolism assay reagent development. |
| CAS No. | 32-1-2056 |
| Enzyme Commission Number | EC 3.2.1.20 |
| Enzyme Source | Human embryonic kidney cell, HEK293-derived human Lysosomal alpha-Glucosidase protein. |
| Reaction | Hydrolysis of terminal, non-reducing (1->4)-linked alpha-D-glucose residues with release of alpha-D-glucose. |
| Activity Definition | Measured by its ability to release glucose from starch under the described conditions. |
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